Biliary Atresia

Case No. 19: Biliary Atresia

Atresia of the extrahepatic biliary tree is biliary atresia.
Occurs due to failure of recanalization of the caudal component of the hepatic diverticulum.
Child presents with progressive jaundice, acholic stools, and firm hepatomegaly.
If the fasting USG of the child with the above symptoms does not show dilated gall bladder, an Intraoperative cholangiogram is the best way to diagnose. Liver biopsy is also suggested.
Treated by a Roux en y hepaticojejunostomy. The outcome is better if operated on within 45-60 days of birth.
Delayed surgery leads to Liver cirrhosis. The child might require a liver transplant in that case.