Case No. 19: Biliary Atresia
- Atresia of the extrahepatic biliary tree is biliary atresia.
- Occurs due to failure of recanalization of the caudal component of the hepatic diverticulum.
- Child presents with progressive jaundice, acholic stools, and firm hepatomegaly.
- If the fasting USG of the child with the above symptoms does not show dilated gall bladder, an Intraoperative cholangiogram is the best way to diagnose. Liver biopsy is also suggested.
- Treated by a Roux en y hepaticojejunostomy. The outcome is better if operated on within 45-60 days of birth.
- Delayed surgery leads to Liver cirrhosis. The child might require a liver transplant in that case.